Year 2022 / Volume 114 / Number 11
Letter
Esophagogastric variceal bleeding as a debut of Caroli’s syndrome

678

DOI: 10.17235/reed.2022.8813/2022

Julia del Río Izquierdo, Clara Ramos Belinchón, Rafael Bañares, Laura Carrión Martín,

Abstract
Caroli's disease is a congenital disease characterized by saccular or cystic dilatations of intrahepatic bile ducts. It is called Caroli’s syndrome (CS) when intrahepatic dilations are associated with congenital hepatic fibrosis. CS is an infrequent cause of gastrointestinal bleeding in young people that should be considered when saccular dilatations of the bile duct are associated with portal hypertension (PHT). We present a rare case with gastrointestinal bleeding as first manifestation of CS: A 13-year-old woman with no relevant medical history was admitted to the hospital with an episode of hematemesis.
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References
1. Bruguera M, Ros E. Enfermedad de Caroli. Gastroenterol Hepatol. 2006;29(8).
2. Desmet VJ. Congenital diseases of intrahepatic bile ducts: Variations on the theme “ductal plate malformation.” Hepatology. 1992;16(4).
3. Shi W, Huang XM, Feng YL, Wang FD, Gao XX, Jiao Y. Factors contributing to diagnostic delay of Caroli syndrome: A single-center, retrospective study. BMC Gastroenterol. 2020;20(1).
4. Yonem O. Clinical characteristics of Caroli’s syndrome. World J Gastroenterol. 2007;13(13).
5. Wang S, Xiao M, Hua L, Jia Y, Chen S, Zhang K. Endoscopic therapy for gastro-oesophageal varices of Caroli’s syndrome: a case report. J Int Med Res. 2019;48(2).
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del Río Izquierdo J, Ramos Belinchón C, Bañares R, Carrión Martín L. Esophagogastric variceal bleeding as a debut of Caroli’s syndrome. 8813/2022


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Publication history

Received: 22/03/2022

Accepted: 30/03/2022

Online First: 29/04/2022

Published: 07/11/2022

Article Online First time: 38 days

Article editing time: 230 days


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