Year 2022 / Volume 114 / Number 12
Letter
Primary intestinal lymphangiectasia: a rare disease as a cause of protein-losing enteropathy

762-763

DOI: 10.17235/reed.2022.8673/2022

Rita González Núñez, Ana Belén Domínguez Carbajo, Laura Alcoba Vega, Jesús Espinel Díez, Santiago Vivas Alegre,

Abstract
Primary intestinal lymphangiectasia is a rare disorder associated with protein-losing enteropathy. The main manifestations are those resulting from hypoalbuminemia. Diagnosis requires the typical endoscopic image of intestinal lymphangiectasia and increased 24-hour fecal alpha-1-antitrypsin clearance. Treatment is basically dietary.
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References
1.Waldmann TA, Steinfeld JL, Dutcher TF et al. The role of the gastrointestinal system in "idiopathic hypoproteinemia". Gastroenterology 1961 9;41:197-207.
2. Brownell JN, Piccoli D. Protein-losing gastroenteropathy. En Lamont JT, Grover S (Ed.). UpToDate [Internet] [Consultado 2021 diciembre 2]. Disponible en https://www.uptodate.com/contents/protein-losing-gastroenteropathy?search=enteropatia%20pierde%20proteinas&source=search_result&selectedTitle=1~83&usage_type=default&display_rank=1
3.Vignes S. Linfangiectasia intestinal primaria. Orphanet [Internet] [consultado 2021 noviembre 15]. Disponible en: https://www.orpha.net/consor4.01/www/cgi-bin/Disease_Search.php?lng=ES&data_id=12030&Disease_Disease_Search_diseaseGroup=linfangiectasia-intestinal-primaria&Disease_Disease_Search_diseaseType=Pat&Enfermedad(es)/grupo%20de%20enfermedades=Linfangiectasia-intestinal-primaria&title=Linfangiectasia%20intestinal%20primaria&search=Disease_Search_Simple.
4. Wu J, Huang Z, Ji M et al. The diagnostic value of capsule endoscopy in children with intestinal lymphangiectasia. Rev Esp Enferm Dig. 2021 Nov;113(11):765-769.
5. Ingle SB, Hinge (Ingle) CR. Primary intestinal lymphangiectasia: Minireview. World J Clin Cases 2014 16; 2(10): 528-533.
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Citation tools
González Núñez R, Domínguez Carbajo A, Alcoba Vega L, Espinel Díez J, Vivas Alegre S. Primary intestinal lymphangiectasia: a rare disease as a cause of protein-losing enteropathy. 8673/2022


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Publication history

Received: 02/02/2022

Accepted: 08/02/2022

Online First: 04/03/2022

Published: 12/12/2022

Article Online First time: 30 days

Article editing time: 313 days


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