Year 2016 / Volume 108 / Number 8
Original
Agenesis of the dorsal pancreas: systematic review of a clinical challenge

479-484

DOI: 10.17235/reed.2016.4474/2016

Javier A. Cienfuegos, Fernando Rotellar, Joseba Salguero, Alberto Benito, José Luis Solórzano, Bruno Sangro,

Abstract
Background: Agenesis of the dorsal pancreas is a rare malformation. Since 1911 and until 2008, 53 cases have been reported. Several authors have recently described the association of this anomaly with neoplasia of the ventral pancreas, thus we performed a systematic review of the literature from 2008 to 2015. Methods: A systematic review of the MedLine and ISI Web of Science Databases from 2008 until 2015 was carried out, and 30 articles which met the inclusion criteria were identified that included a total of 53 patients: 7 children and 46 adults. Conclusions: Although dorsal pancreatic agenesis is a rare malformation, given its association with non-alcoholic pancreatitis and neoplasia of the residual pancreas, physicians should maintain an expectant attitude.
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A. Cienfuegos J, Rotellar F, Salguero J, Benito A, Solórzano J, Sangro B, et all. Agenesis of the dorsal pancreas: systematic review of a clinical challenge. 4474/2016


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Publication history

Received: 30/05/2016

Accepted: 03/06/2016

Online First: 29/07/2016

Published: 29/07/2016

Article Online First time: 60 days

Article editing time: 60 days


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