Year 2024 / Volume 116 / Number 11
Letter
Abernethy syndrome as a cause of liver transplantation

646-647

DOI: 10.17235/reed.2024.10561/2024

Angélica Blanco Rodríguez, Dora Gómez Pasantes, Mónica Torres Díaz, Irene Aguirrezabalaga Martínez, Carla Madarro Pena, Aloia Guerreiro Caamaño, Javier Aguirrezabalaga González, Manuel Gómez Gutiérrez,

Abstract
Congenital portosystemic shunts are rare abnormalities in which blood flow from the liver is diverted to the systemic circulation. We would like to present the case of a 48-year-old male, during his neurological follow-up he was diagnosed with a congenital intrahepatic portosystemic shunt. Embolization of the portosystemic communicating veins was attempted on two occasions, but without success. Due to the poor clinical course, the patient was presented to our transplant committee and a liver transplant was decided upon.
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References
Castro Rodríguez J, Rodríguez Perálvarez ML, Montero-Álvarez JL. Diagnosis and management of Abernethy syndrome. Rev Esp Enferm Dig. 2024 Jan;116(1):1-6. doi: 10.17235/reed.2023.9781/2023. PMID: 37522317
Papamichail M, Pizanias M, Heaton N. Congenital portosystemic venous shunt. Eur J Pediatr 2018; 177:285-294
Watanabe A. Portal-systemic encephalopathy in non-cirrhotic patients: Classification of clinical types, diagnosis and treatment.  Journal of Gastroenterology and Hepatology, 2000; 15: 969-979
Benedict M, Rodriguez-Davalos M, Emre S et al. Congenital Extrahepatic Portosystemic Shunt (Abernethy Malformation Type Ib) With Associated Hepatocellular Carcinoma: Case Report and Literature Review. Pediatr Dev Pathol 2017;20(4):354-362
Alvi A, Pichardo J, et al. An interesentig case of congenital intrahepatic porto-hepatic shunt as a cause of unexplained encephalopathy. Cureus 2020; 12(4)
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Citation tools
Blanco Rodríguez A, Gómez Pasantes D, Torres Díaz M, Aguirrezabalaga Martínez I, Madarro Pena C, Guerreiro Caamaño A, et all. Abernethy syndrome as a cause of liver transplantation. 10561/2024


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Publication history

Received: 26/05/2024

Accepted: 07/06/2024

Online First: 05/07/2024

Published: 11/11/2024

Article Online First time: 40 days

Article editing time: 169 days


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