Year 2017 / Volume 109 / Number 5
Case Report
Intrahepatic clear cell cholangiocarcinoma - An uncommon histologic subtype: case report and literature review

382-385

DOI: 10.17235/reed.2017.4239/2016

Samuel Raimundo Fernandes, Cilénia Baldaia, Hugo Pinto Marques, Francisco Tortosa, Fernando Ramalho,

Abstract
Clear-cell cholangiocarcinoma is a very uncommon variant of cholangiocarcinoma with a largely unknown natural history and prognosis. We report a case of a 51-year-old previously healthy woman presenting with a large liver nodule found on routine imaging. Needle biopsy of the lesion suggested a non-hepatocellular carcinoma. After extensive workup for other primary neoplasms, the patient underwent a partial hepatectomy. Histopathology was compatible with a moderately differentiated clear-cell cholangiocarcinoma. There was no evidence of liver disease in the remaining tissue. The patient underwent chemotherapy and remains in clinical remission after two years.
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Fernandes S, Baldaia C, Pinto Marques H, Tortosa F, Ramalho F. Intrahepatic clear cell cholangiocarcinoma - An uncommon histologic subtype: case report and literature review. 4239/2016


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Publication history

Received: 30/01/2016

Accepted: 01/10/2016

Online First: 03/02/2017

Published: 03/05/2017

Article revision time: 241 days

Article Online First time: 370 days

Article editing time: 459 days


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