Year 2023 / Volume 115 / Number 7
Letter
Budd-Chiari syndrome in Behçet’s disease

395-396

DOI: 10.17235/reed.2022.9267/2022

Daniel Alvarenga Fernandes, Carlos Eduardo Garcez Teixeira, Zoraida Sachetto, Fabiano Reis,

Abstract
A 36-year-old man was admitted to the emergency department due to a 30-day history of abdominal distention and epigastralgia. He had described a non-intentional 10kg weight loss, dry cough, and fever 6 months before his admission. He had a history of tobacco and cocaine abuse and reported recurrent oral and genital ulcers. Physical examination showed an extensive area of venous collateral circulation on the abdominal wall, hepatomegaly, signs of a moderate ascites, and lower limb edema. Liver and renal function tests were normal. The ascitic fluid analysis did not show an inflammatory or infectious pattern. Upper flexible endoscopy revealed esophageal fine-caliber varices and colonoscopy showed an isolated terminal ileal ulcer. Abdominal imaging revealed hepatomegaly, voluminous ascites, and thrombosis of hepatic veins, inferior and superior vena cava (Figure 1). Infections and coagulation or lymphoproliferative disorders were excluded. Thereafter, the diagnosis of Budd-Chiari Syndrome in Behçet disease was established and immunosuppression treatment was started with good initial clinical evolution.
Share Button
New comment
Comments
No comments for this article
References
1. Vieira RM, do Nascimento FBP, Barbosa Júnior AA, et al. Spectrum of central nervous system involvement in rheumatic diseases: pictorial essay. Radiol Bras. 2018;51(4):262-267.
2. International Team for the Revision of the International Criteria for Behçet's Disease (ITR-ICBD). The International Criteria for Behçet's Disease (ICBD): a collaborative study of 27 countries on the sensitivity and specificity of the new criteria. J Eur Acad Dermatol Venereol. 2014;28(3):338-47.
3. Seyahi E. Behçet's disease: How to diagnose and treat vascular involvement. Best Pract Res Clin Rheumatol. 2016;30(2):279-295.
4. Hatemi G, Christensen R, Bang D, et al. 2018 update of the EULAR recommendations for the management of Behçet's syndrome. Ann Rheum Dis. 2018;77(6):808-818.
5. Emmi G, Bettiol A, Silvestri E, et al. Vascular Behçet's syndrome: an update. Intern Emerg Med. 2019;14(5):645-652.
Citation tools
Alvarenga Fernandes D, Garcez Teixeira C, Sachetto Z, Reis F. Budd-Chiari syndrome in Behçet’s disease. 9267/2022


Download to a citation manager

Download the citation for this article by clicking on one of the following citation managers:

Metrics
This article has received 1393 visits.
This article has been downloaded 89 times.

Statistics from Dimensions


Statistics from Plum Analytics

Publication history

Received: 07/10/2022

Accepted: 10/10/2022

Online First: 20/10/2022

Published: 06/07/2023

Article Online First time: 13 days

Article editing time: 272 days


Share
This article hasn't been rated yet.
Reader rating:
Valora este artículo:




Asociación Española de Ecografía Digestiva Sociedad Española de Endoscopia Digestiva Sociedad Española de Patología Digestiva
The Spanish Journal of Gastroenterology is the official organ of the Sociedad Española de Patología Digestiva, the Sociedad Española de Endoscopia Digestiva and the Asociación Española de Ecografía Digestiva
Cookie policy Privacy Policy Legal Notice © Copyright 2023 y Creative Commons. The Spanish Journal of Gastroenterology